Familial cerebral amyloidosis and spongiform encephalopathy.

  title={Familial cerebral amyloidosis and spongiform encephalopathy.},
  author={Jan Adam and Timothy John Crow and L. W. Duchen and Francesco Scaravilli and E G S Spokes},
  journal={Journal of neurology, neurosurgery, and psychiatry},
  volume={45 1},
Clinical and neuropathological investigations are presented of the "W" family in which there is a dominant inheritance of slowly progressive cerebellar ataxia and dementia. The disease is of insidious onset and its average duration more than 4 years. Pathological findings included amyloid deposition in cerebellar and cerebral tissue; vascular amyloid in one… CONTINUE READING