Familial Occurrence of Cleidocranial Dysostosis: A Case Report

  title={Familial Occurrence of Cleidocranial Dysostosis: A Case Report},
  author={Gauri Shailesh Lele and Bhagyashree Salunkhe},
Cleidocranial dysostosis is a rare congenital skeletal disorder, associated with total or partial absence of clavicles, delayed closure of cranial fontanelles and brachycephalic skull. There is delayed exfoliation of primary dentition and eruption of permanent teeth. Presence of multiple supernumerary teeth and morphologic abnormalities of the maxilla and mandible are also observed. The incidence of this autosomal dominant disorder is reported as 1:10,00,000 and the prevalence is 0.5:1,00,000… CONTINUE READING