Familial Aquagenic Urticaria and Bernard-Soulier Syndrome

@article{Pitarch2005FamilialAU,
  title={Familial Aquagenic Urticaria and Bernard-Soulier Syndrome},
  author={Gerard Pitarch and Arantxa Torrijos and Teresa Mart{\'i}nez-Mench{\'o}n and Jose S{\'a}nchez-Carazo and Jos{\'e} Miguel Fortea},
  journal={Dermatology},
  year={2005},
  volume={212},
  pages={96 - 97}
}
Department of Dermatology, Valencia University General Hospital, Valencia , Spain of age and subsequently gradually worsened. The two younger siblings had Bernard-Soulier syndrome. A challenge test could be performed in the 26-year-old sibling, proving positive for tap water at room temperature, and for hot and cold water – though the lesions were less numerous than in the case of the older patient. A challenge test could not be performed with the 24-year-old sibling. The mother of the 3 women… 

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