False positive reporting of Hirschsprung's disease in Alaska: an evaluation of Hirschsprung's disease surveillance, birth years 1996-2007.

@article{Schoellhorn2009FalsePR,
  title={False positive reporting of Hirschsprung's disease in Alaska: an evaluation of Hirschsprung's disease surveillance, birth years 1996-2007.},
  author={Janine Schoellhorn and Sandra Collins},
  journal={Birth defects research. Part A, Clinical and molecular teratology},
  year={2009},
  volume={85 11},
  pages={
          914-9
        }
}
BACKGROUND Hirschsprung's disease (HSCR) is a potentially fatal congenital intestinal obstruction syndrome. For birth years 1996-2002, reported HSCR prevalence in Alaska was approximately six times higher than the national estimate of two per 10,000 live births. In 2008 we completed a case verification study of HSCR reported to the Alaska Birth Defects Registry (ABDR) to verify prevalence and evaluate sensitivity and predictive value of HSCR surveillance. METHODS We abstracted medical records… 
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