Extrahepatic biliary atresia and caudal regression syndrome in an infant of a diabetic mother.

@article{Herrmann2004ExtrahepaticBA,
  title={Extrahepatic biliary atresia and caudal regression syndrome in an infant of a diabetic mother.},
  author={Jochen Herrmann and Martin Brauer and Ianina Scheer and Winfried Barthlen and Christoph B{\"u}hrer},
  journal={Journal of pediatric surgery},
  year={2004},
  volume={39 1},
  pages={
          E20-2
        }
}
Although most cases of extrahepatic biliary atresia are thought to result from perinatal obliterating inflammation, some are associated with a faulty morphogenesis. The authors report on a baby girl of a mother with ill-managed insulin-dependent diabetes mellitus. The baby presented with sacro-coccygeal agenesis, clubfoot, and ano-urinary incontinence. In addition, there was polysplenia, no inferior vena cava, and the portal vein was grossly distorted. Progressive conjugated hyperbilirubinemia… CONTINUE READING