Esthesioneuroblastoma in Maffucci’s syndrome

  title={Esthesioneuroblastoma in Maffucci’s syndrome},
  author={Sobha Kurian and Esmer Ertan and Barbara S. Ducatman and Edward B. Crowell and Christopher H. Rassekh},
  journal={Skeletal Radiology},
Maffucci’s syndrome consists of multiple cutaneous hemangiomas, dyschondroplasia, and enchondromas with potential for malignant change. We report a case of a 33-year-old man with Maffucci’s syndrome who presented with a several month history of nasal congestion, facial pain, and diminished vision in his left eye. Radiological studies showed a large soft tissue mass centered in the sinonasal area, extending bilaterally into maxillary sinuses and orbits with compression of left optic nerve… CONTINUE READING


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