Erythropoietic protoporphyria. An overview with emphasis on the liver.

  title={Erythropoietic protoporphyria. An overview with emphasis on the liver.},
  author={Leo Meerman},
  journal={Scandinavian journal of gastroenterology. Supplement},
  • Leo Meerman
  • Published 2000 in
    Scandinavian journal of gastroenterology…
BACKGROUND Erythropoietic protoporphyria (EPP) is an inherited disorder of heme synthesis, causing excess of protoporphyrin in blood, skin, liver and other organs. Protoporphyrin accumulation causes rapidly progressive liver failure in a minority of patients. Many questions concerning liver disease in EPP patients remain to be solved. METHODS Review and update of the literature on EPP, protoporphyrin and hepatic involvement. RESULTS The protoporphyrin molecule can be excited by absorbing… CONTINUE READING