Erdheim-Chester disease of the central nervous system. Report of two cases.

@article{Babu1997ErdheimChesterDO,
  title={Erdheim-Chester disease of the central nervous system. Report of two cases.},
  author={Ramesh P Babu and Thomas A. Lansen and Amy Chadburn and S S Kasoff},
  journal={Journal of neurosurgery},
  year={1997},
  volume={86 5},
  pages={888-92}
}
The authors report two cases of Erdheim-Chester disease (ECD), an illness of unknown pathogenesis. Generally, this disease process involves the metaphyseal and diaphyseal portions of the long bones, the lungs, and the retroperitoneum; however, other tissues may be involved including the central nervous system (CNS). To date only two cases of CNS-related ECD have been reported. The present report adds to the literature by documenting two more recent cases of ECD involving the CNS. The clinical… CONTINUE READING