Erdheim-Chester disease in a child presenting with multiple jaw lesions.

  title={Erdheim-Chester disease in a child presenting with multiple jaw lesions.},
  author={Hitoshi Nagatsuka and Phuu Pwint Han and Koji Taguchi and Hidetsugu Tsujigiwa and Mehmet Gunduz and Joji Fukunaga and Toshio Sugahara and J Asaumi and Noriyuki Nagai},
  journal={Journal of oral pathology & medicine : official publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology},
  volume={34 7},
BACKGROUND Erdheim-Chester disease is a rare histiocytic disease entity related to juvenile xanthogranuloma. It is a systemic condition, usually occurs in adult, characterized by infiltration of foamy histiocytes within the bone and soft tissues. METHODS AND RESULTS We report a case of 13-year-old female patient who first presented with multiple osteolytic lesions of the jaws followed by bilateral symmetrical bone lesions affecting the lower extremities, as well as brain and abdominal… CONTINUE READING