Epidemiology of Severe Myoclonic Epilepsy of Infancy

@article{Hurst1990EpidemiologyOS,
  title={Epidemiology of Severe Myoclonic Epilepsy of Infancy},
  author={Daniel L. Hurst},
  journal={Epilepsia},
  year={1990},
  volume={31}
}
  • D. Hurst
  • Published 1 August 1990
  • Medicine
  • Epilepsia
Summary: Severe myoclonic epilepsy of infancy (SMEI) is a newly recognized epileptic syndrome. It is characterized by multiple febrile seizures, often prolonged, subsequent development of uncontrollable mixed‐myoclonic seizures, and, eventually, psychomotor retardation. Drugs for myoclonic epilepsy–valproate (VPA), the suximides, and the benzodiazepines–have been shown to be useful in SMEI. Among children with seizures in the National Institute of Neurological and Communicative Disorders and… 
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