Endolymphatic Sac Tumor: Unique Features of two Cases and Review of the Literature

  title={Endolymphatic Sac Tumor: Unique Features of two Cases and Review of the Literature},
  author={Mauro Ferreira and Iman Feiz-Erfan and Joseph M. Zabramski and Robert F. Spetzler and Stephen W. Coons and Mark C. Preul},
  journal={Acta Neurochirurgica},
 Endolymphatic sac tumors (EST) are rare intracranial tumors originating from the pars rugosa of the endolymphatic sac. Although typically described as histologically nonaggressive lesions, nevertheless they are termed adenocarcinomas and often become locally invasive. We report two patients with histologically proven EST with unique clinical features: the first pediatric case of an EST in an 11-year-old patient whose complaints started at the age of seven; and, a second patient, a 43-year-old… CONTINUE READING
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