Effective treatment of Kimura’s disease with leflunomide in combination with glucocorticoids

  title={Effective treatment of Kimura’s disease with leflunomide in combination with glucocorticoids},
  author={Lie Dai and Xiu-ning Wei and Dong-hui Zheng and Ying-Qian Mo and Frank Pessler and Bai-yu Zhang},
  journal={Clinical Rheumatology},
Kimura’s disease (KD) is a rare, benign, chronic inflammatory disease which typically presents as persisting or recurring tumor-like lesions in the head and neck area that can be easily misdiagnosed. We report one patient with KD treated with leflunomide in combination with glucocorticoids and analyzed the literature on treatment of KD. The patient had a recurrent mass in the left upper arm with eosinophilia and elevated serum IgE but no renal involvement. The clinical manifestations improved… 

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Kimura's Disease.

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The beneficial effect of cetirizine—a selective H1 receptor blocker—in a patient with Kimura’s disease is described.

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The case of a 10-year-old boy with a past history of steroid responsive, frequently relapsing nephrotic syndrome who developed a right submandibular swelling and eosinophilia is presented.

Kimura disease: review of the literature

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Kimura's disease presenting with a giant suspensory tumor and associated with membranoproliferative glomerulonephritis.

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