Dramatic and sustained responsiveness of pulmonary Langerhans cell histiocytosis-associated pulmonary hypertension to vasodilator therapy

Abstract

Pulmonary Langerhans cell histiocytosis (PLCH) is an uncommon diffuse lung disease characterized by the abnormal accumulation of Langerhans' cells around small airways and other distal lung compartments. Although pulmonary hypertension (PH) is a frequent complication of PLCH, the role of advanced PH therapies for PLCH-related PH is not well-established. We… (More)
DOI: 10.1016/j.rmcr.2014.11.005

Topics

2 Figures and Tables

Cite this paper

@inproceedings{May2015DramaticAS, title={Dramatic and sustained responsiveness of pulmonary Langerhans cell histiocytosis-associated pulmonary hypertension to vasodilator therapy}, author={Adam M May and Garvan Kane and Eunhee Yi and Robert Frantz and Robert Vassallo}, booktitle={Respiratory medicine case reports}, year={2015} }