Discordant sexual identity in some genetic males with cloacal exstrophy assigned to female sex at birth.

@article{Reiner2004DiscordantSI,
  title={Discordant sexual identity in some genetic males with cloacal exstrophy assigned to female sex at birth.},
  author={William George Reiner and John P. Gearhart},
  journal={The New England journal of medicine},
  year={2004},
  volume={350 4},
  pages={
          333-41
        }
}
  • W. Reiner, J. Gearhart
  • Published 22 January 2004
  • Medicine, Psychology
  • The New England journal of medicine
BACKGROUND Cloacal exstrophy is a rare, complex defect of the entire pelvis and its contents that occurs during embryogenesis and is associated with severe phallic inadequacy or phallic absence in genetic males. For about 25 years, neonatal assignment to female sex has been advocated for affected males to overcome the issue of phallic inadequacy, but data on outcome remain sparse. METHODS We assessed all 16 genetic males in our cloacal-exstrophy clinic at the ages of 5 to 16 years. Fourteen… 

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