Digital clubbing in primary intestinal lymphangiectasia: a case report

@article{Wiedermann2010DigitalCI,
  title={Digital clubbing in primary intestinal lymphangiectasia: a case report},
  author={Christian Josef Wiedermann and Michael Kob and Stefano Benvenuti and Rodolfo Carella and Lucio Lucchin and Lucia Piazzi and Fausto Chilovi and Guido Mazzoleni},
  journal={Wiener Medizinische Wochenschrift},
  year={2010},
  volume={160},
  pages={431-436}
}
ZusammenfassungDie primäre intestinale Lymphangiektasie ist eine seltene Erkrankung, die durch erweiterte Lymphgefäße der Dünndarmschleimhaut gekennzeichnet ist und zum Verlust von Lymphe in das Darmlumen führt. Die so entstehende Eiweiß-Verlust-Enteropathie ist labordiagnostisch durch Lymphopenie, Hypoalbuminämie und Hypogammaglobulinämie gekennzeichnet. Symptome beginnen für gewöhnlich in der frühen Kindheit. Hier berichten wir über einen Fall von Hypoalbuminämie und Hypogammaglobulinämie bei… 
4 Citations
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Surgical small-bowel resection is useful in the rare cases with segmental and localized intestinal lymphangiectasia and a prolonged clinical and biological follow-up is recommended.
Primary intestinal lymphangiectasia: Minireview.
TLDR
Recently double-balloon enteroscopy and biopsy in combination can be used as an effective diagnostic tool to hit the correct diagnosis of primary idiopathic intestinal lymphangiectasia.
Primary intestinal lymphangiectasia in an adult patient: A case report and review of literature
TLDR
PIL can be the reason for cryptogenic hypoalbuminemia, hypogammaglobulinemi, and lymphopenia in adulthood in adulthood, and the association with female hormone status warrants further investigation.
Endoscopic and Imaging Findings in Protein-losing Enteropathy
TLDR
DBE with pathologic findings of biopsy specimens was useful for the differential diagnosis of PLE and noninvasive VCE might be preferable and useful for screening and follow-up of Ple without stricture.

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TLDR
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T H I S title is used to describe a nail dystrophy which although not rare has received very little mention in earlier literature. The main features of the syndrome are slow growing disrolourod nails
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