Digestive tract symptoms in congenital langerhans cell histiocytosis: a fatal condition in an illness usually considered benign.

@article{VetterLaracy2014DigestiveTS,
  title={Digestive tract symptoms in congenital langerhans cell histiocytosis: a fatal condition in an illness usually considered benign.},
  author={Susanne Irene Christa Vetter-Laracy and Jos{\'e} Antonio Salinas and Ana Mart{\'i}n-Santiago and Mercedes Guibelalde and Pere-Ramon Balliu},
  journal={Journal of pediatric hematology/oncology},
  year={2014},
  volume={36 6},
  pages={426-9}
}
INTRODUCTION Congenital Langerhans cell histiocytosis is usually limited to cutaneous lesions and has a good prognosis. In rare cases of gut involvement, mortality is high and early and aggressive treatment essential. MATERIALS AND METHODS We report a case of histiocytosis in a newborn with bowel involvement, and performed a literature review of 13 similar cases worldwide documented between 1973 and 2008. RESULTS Skin eruptions are usually the initial symptoms at birth. Bloody stools or… CONTINUE READING