Diagnostic and surgical challenge: middle ear dermoid cyst in 12 month old with branchio-oto-renal syndrome and multiple middle-ear congenital anomalies.

@article{Johnston2011DiagnosticAS,
  title={Diagnostic and surgical challenge: middle ear dermoid cyst in 12 month old with branchio-oto-renal syndrome and multiple middle-ear congenital anomalies.},
  author={Douglas R. Johnston and Kenneth Whittemore and Dennis Poe and Caroline D Robson and Antonio R. Perez-Atayde},
  journal={International journal of pediatric otorhinolaryngology},
  year={2011},
  volume={75 10},
  pages={
          1341-5
        }
}
Described is the first case report, to our knowledge, of a middle-ear dermoid in a child with branchio-oto-renal (BOR) syndrome. Radiographic, pathologic, and intraoperative figures are shown. This was a diagnostic and surgical challenge as the presentation was similar to a congenital cholesteatoma and the child had numerous significant temporal bone abnormalities. After the intraoperative findings suggested a non-destructive process, the treatment strategy was altered. This case reiterates the… CONTINUE READING