Delayed enhancement of pelvic lymphangiomyoma associated with lymphangioleiomyomatosis on MR imaging (2005:9b)

Abstract

Lymphangioleiomyomatosis (LAM) is a rare disorder characterized by proliferation of smooth muscle cells in the lung parenchyma and lymphatic system [1]. The proliferating cells, namely LAM cells, are characteristically stained with monoclonal antibodies for HMB-45 [1]. Lymphangiomyoma, a cystic mass produced as a result of lymphatic obstruction by proliferating smooth muscle cells in the lymphatic system [2] is observed in 16–21% of patients with LAM [2–4] and is the third most common form of extrapulmonary involvement of LAM after renal angiomyolipoma and enlarged abdominal lymph nodes [3]. We describe a woman who was admitted to our hospital for increasing abdominal distention. LAM was diagnosed and a pelvic lymphagiomyoma was revealed. The radiological features of lymphangiomyoma are discussed, with emphasis on magnetic resonance (MR) images.

DOI: 10.1007/s00330-005-2860-4

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Cite this paper

@article{Maeda2005DelayedEO, title={Delayed enhancement of pelvic lymphangiomyoma associated with lymphangioleiomyomatosis on MR imaging (2005:9b)}, author={Eriko Maeda and Masaaki Akahane and Yusuke Inoue and Takeyuki Watadani and Daisuke Jo and Jun Kato and Manabu Minami and Kuni Ohtomo}, journal={European Radiology}, year={2005}, volume={15}, pages={2528-2531} }