Delayed Enhancement Cardiac Magnetic Resonance Imaging in Propionic Acidemia


We report on cardiomyopathy in propionic acidemia (PA) diagnosed using delayed-enhancement cardiac magnetic imaging (DECM) in a 27-year-old woman. DECM demonstrated hyperenhancement at the lateral wall of the left ventricle, suggesting myocardial changes occurring after a metabolic crisis, which improved during the convalescent period. DECM was useful for… (More)
DOI: 10.1007/s00246-010-9723-8


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