Deafness due to bilateral endolymphatic sac tumours in a case of von Hippel-Lindau syndrome.

@article{Kempermann1996DeafnessDT,
  title={Deafness due to bilateral endolymphatic sac tumours in a case of von Hippel-Lindau syndrome.},
  author={Gerd Kempermann and Hartmut P. H. Neumann and Rudolf Scheremet and Benedikt Volk and W. Mann and Joachim Gilsbach and Roland Laszig},
  journal={Journal of neurology, neurosurgery, and psychiatry},
  year={1996},
  volume={61 3},
  pages={
          318-20
        }
}
A case of bilateral endolymphatic sac tumours is reported. In a patient with von Hippel-Lindau syndrome, tumour growth in the right cerebellopontine angle caused deafness. The tumour was removed and classified as a metastasis from a thyroid carcinoma. However, on thyroidectomy no primary neoplasm could be found. Eight years later a similar tumour was operated on in the left petrosal bone. Histological appearance, immunocytochemical findings, and the clinical context gave evidence that the… CONTINUE READING
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