Dandy Walker Syndrome with Tessier 7 Cleft-a Rare Case Report and a Surgical Note on the Use of Vermilion Flap and Lazy W-Plasty

@article{Dhupar2012DandyWS,
  title={Dandy Walker Syndrome with Tessier 7 Cleft-a Rare Case Report and a Surgical Note on the Use of Vermilion Flap and Lazy W-Plasty},
  author={Vikas Dhupar and Praveen Satish Kumar and Francis Akkara and Ananth Kumar},
  journal={Journal of Maxillofacial and Oral Surgery},
  year={2012},
  volume={11},
  pages={368-370}
}
The Dandy-Walker syndrome is a malformation of the brain that involves the mal-development of the cerebellum, associated with a cystic enlargement of this area, and frequently hydrocephalus. This malformation occurs in ~1 in 30,000 babies. It is seen mostly in females. Developmental anomalies like cleft lip, cleft palate, and cardiac malformation, orthopaedic and urinary structural abnormalities may also occur in 30% of the individuals. We report a case of Dandy Walker syndrome with Tessier 7… 
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A rare case of accessory maxilla: a case report and literature review of Tessier no. 7 clefts

The presence of an accessory maxilla with supernumerary teeth in a patient with bilateral Tessier no. 7 clefts is described, which is extremely rare and may influence patient prognosis and management.

Prenatal Diagnosis of Tessier 7 Cleft in a Case of Femoral Hypoplasia-Unusual Facies Syndrome with Associated Absent Fibula and Digit Abnormalities

A 32-year-old white, gravida 1, underwent fetal karyotyping for high risk of common trisomies due to nuchal translucency (NT) > 99th centile and multiple sonographic markers of skeletal dysplasia were characterized by bilateral femoral hypoplasia, curved tibia, and absent fibula.

The Most Common Comorbidities in Dandy-Walker Syndrome Patients: A Systematic Review of Case Reports

The spread of comorbidities calls for early diagnosis and multidisciplinary research and practice, especially as many cases remain clinically asymptomatic for years.

Health Problems of Children with the Dandy-Walker Syndrome

There is a large number of health problems indicating massive needs in care and hence, they require treatment by many specialists, Consequently, families of children with Dandy-Walker syndrome should be covered by active counselling on problems arising both from basic sickness unit and the coexistent ones.

Biallelic mutations in EXOC3L2 cause a novel syndrome that affects the brain, kidney and blood

It is proposed that biallelic EXOC3L2 mutations lead to a novel syndrome that affects hindbrain development, kidney and possibly the bone marrow.

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