Current and Future Treatments for Malignant Pheochromocytoma and Sympathetic Paraganglioma

  title={Current and Future Treatments for Malignant Pheochromocytoma and Sympathetic Paraganglioma},
  author={C. Jimenez and E. Rohren and M. Habra and T. Rich and Paola Jim{\'e}nez and M. Ayala-Ramirez and E. Baudin},
  journal={Current Oncology Reports},
  • C. Jimenez, E. Rohren, +4 authors E. Baudin
  • Published 2013
  • Medicine
  • Current Oncology Reports
  • Pheochromocytomas (PHs) and sympathetic paragangliomas (SPGs) are rare neuroendocrine tumors. Approximately 17 % of these tumors are malignant, but because no molecular or histologic markers for malignancy exist, patients are often diagnosed with malignant PHs or SPGs after unresectable disease has formed. Patients with progressive metastatic tumors and overwhelming symptoms are currently treated with systemic chemotherapy and radiopharmaceutical agents such as metaiodobenzylguanidine. These… CONTINUE READING
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