Cranio-orbital-temporal neurofibromatosis with cerebral hemiatrophy presenting as an intraoral mass: a case report.

@article{Avcu2009CranioorbitaltemporalNW,
  title={Cranio-orbital-temporal neurofibromatosis with cerebral hemiatrophy presenting as an intraoral mass: a case report.},
  author={Nihal Avcu and Ozden Kansu and Serdar Uysal and Hilmi Kansu},
  journal={Journal of the California Dental Association},
  year={2009},
  volume={37 2},
  pages={
          119-21
        }
}
Neurofibromatosis, NF, is a group of genetic disorders that primarily affect the cell growth of neural tissues. Cranio-orbital-temporal neurofibromatosis is an uncommon subtype of neurofibromatosis characterized by neurofibromas, cranial defects, and specific bone lesions. This case report presents the signs of cranial defects in a 24-year-old Caucasian woman with type 1 NF. Mandibular malformations due to NF and dental defects caused by intraoral masses and radiographic images are presented.