Cowden syndrome and Lhermitte-Duclos disease.

  title={Cowden syndrome and Lhermitte-Duclos disease.},
  author={Steffen Albrecht and Richard M. Haber and Jerry Clay Goodman and Madeleine Duvic},
  volume={70 4},
BACKGROUND Cowden syndrome (CS) is a rare but underdiagnosed autosomal dominant condition also known as "multiple hamartoma-neoplasia syndrome." Patients have multiple tricholemmomas (a type of benign skin appendage tumor) and oral papillomatosis and cutaneous keratoses. They often have goiter, gastrointestinal polyps, and hamartomatous soft tissue lesions. Breast cancer affects approximately one third of women with CS. Lhermitte-Duclos disease (LDD) is a peculiar proliferation of abnormal… CONTINUE READING


Publications citing this paper.
Showing 1-10 of 29 extracted citations

Cowden's syndrome. Case report, with reference to an affected family.

Medicina oral, patologia oral y cirugia bucal • 2006
View 7 Excerpts
Highly Influenced

Oral presentation of 10 patients with Cowden syndrome.

Oral surgery, oral medicine, oral pathology and oral radiology • 2014
View 1 Excerpt

Similar Papers

Loading similar papers…