Cor pulmonale and acute liver necrosis, due to upper airway obstruction as part of pycnodysostosis

Abstract

A male patient with pycnodysostosis suffered from chronic respiratory insufficiency and pulmonary hypertension. This was caused by concomitant upper airway obstruction, resulting from a low implanted uvula and a long soft palate, in combination with glossoptosis and retrognathia due to the flattened mandibular angles. An inter-current respiratory infection… (More)
DOI: 10.1007/BF00572773

5 Figures and Tables

Topics

  • Presentations referencing similar topics