Corpus ID: 22905609

Congenital stationary night blindness: an animal model.

@article{Witzel1978CongenitalSN,
  title={Congenital stationary night blindness: an animal model.},
  author={Donald A. Witzel and E. Smith and R. D. Wilson and Gustavo D Aguirre},
  journal={Investigative ophthalmology \& visual science},
  year={1978},
  volume={17 8},
  pages={
          788-95
        }
}
Electroretinographic studies of myctalopic Appaloosa horses demonstrated photopic and scotopic abnormalities similar to those in humans with congenital stationary night blindness (CSNB) of the Schubert-Bornschein type. The phototopic abnormalities consisted of reduced b-wave amplitudes and slower than normal b-wave implict time. The dark-adapted ERG's consisted of a simple negative potential; the scotopic b-wave was nonrecordable. However, a normal c-wave was present in the dark-adapted… Expand
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