Congenital pulmonary lymphangiectasis: report of an autopsy case masquerading as pulmonary interstitial emphysema.

@article{Yamada2010CongenitalPL,
  title={Congenital pulmonary lymphangiectasis: report of an autopsy case masquerading as pulmonary interstitial emphysema.},
  author={Sohsuke Yamada and Masanori Hisaoka and Tetsuo Hamada and Shunsuke Araki and Mika Shiraishi},
  journal={Pathology, research and practice},
  year={2010},
  volume={206 7},
  pages={522-6}
}
We describe the clinicopathologic features of a case of congenital pulmonary lymphangiectasis (CPL). A male Japanese infant born prematurely at 34 weeks of gestation developed a severe moaning sound, dyspnea, and prominent respiratory acidosis about 10min after delivery. A chest X-ray film showed bilateral frosted glass-like infiltrates with an air bronchogram and an air leak around the cardiac shadow, suggesting pneumomediastinum. The patient died of hypoxemic respiratory failure 13h after… CONTINUE READING

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