Congenital long QT syndrome with functionally impaired atrioventricular conduction: successful treatment by mexiletine and propranolol.

@article{Yao2002CongenitalLQ,
  title={Congenital long QT syndrome with functionally impaired atrioventricular conduction: successful treatment by mexiletine and propranolol.},
  author={Chih-Ta Yao and Jieh-Neng Wang and Yu-Chien Tsai and Chia-Shiang Lin and Jing-ming Wu},
  journal={Journal of the Formosan Medical Association = Taiwan yi zhi},
  year={2002},
  volume={101 4},
  pages={291-3}
}
Congenital long QT syndrome (LQTS) with atrioventricular block is a rare and malignant arrhythmia, which usually responds poorly to traditional beta-blocker therapy. We describe a male neonate with LQTS with ventricular tachycardia and 2:1 atrioventricular block. This patient's sister had similar presentation and died suddenly at the age of 8 months despite beta-blocker and pacemaker therapy. Our patient responded to a combination of sodium channel blocker (mexiletine) and beta-blocker… CONTINUE READING

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