Congenital alveolar capillary dysplasia: rare cause of persistent pulmonary hypertension.

  title={Congenital alveolar capillary dysplasia: rare cause of persistent pulmonary hypertension.},
  author={Sibylle Haraida and Helmut Lochbuehler and Alfred Heger and Andreas Nerlich and Jacques Diebold and Irmgard Wiest and Josef Mueller-Hoecker and Udo Loehrs},
  journal={Pediatric pathology & laboratory medicine : journal of the Society for Pediatric Pathology, affiliated with the International Paediatric Pathology Association},
  volume={17 6},
We report on a rare case of fatal congenital alveolar capillary dysplasia. The newborn boy of a 37 weeks' normal gestation suffered from persistent pulmonary hypertension without any cardiovascular malformation and died at the age of 4 weeks despite intensive treatment. The autopsy tissue was examined histologically, immunohistochemically, and ultrastructurally. Moreover, a three-dimensional tissue reconstruction based on serial sections was performed comparing the affected lung with normal… CONTINUE READING


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