Cone degeneration is triggered by the absence of USH1 proteins but prevented by antioxidant treatments

@inproceedings{Trouillet2018ConeDI,
  title={Cone degeneration is triggered by the absence of USH1 proteins but prevented by antioxidant treatments},
  author={Alix Trouillet and {\'E}lisabeth Dubus and Julie D{\'e}gardin and Amrit Estivalet and Ivana Ivkovi{\'c} and David Godefroy and Diego Garc{\'i}a-Ayuso and Manuel Simonutti and Iman Sahly and Jos{\'e} Alain Sahel and Aziz El-Amraoui and Christine Petit and Serge Picaud},
  booktitle={Scientific Reports},
  year={2018}
}
Usher syndrome type 1 (USH1) is a major cause of inherited deafness and blindness in humans. The eye disorder is often referred to as retinitis pigmentosa, which is characterized by a secondary cone degeneration following the rod loss. The development of treatments to prevent retinal degeneration has been hampered by the lack of clear evidence for retinal… CONTINUE READING