Complete androgen insensitivity syndrome with persistent Mullerian derivatives: A case report

@article{Menakaya2005CompleteAI,
  title={Complete androgen insensitivity syndrome with persistent Mullerian derivatives: A case report},
  author={Uche A. Menakaya and Jonathan Umezuluike Aligbe and Pius Ehiawaguan Iribhogbe and F. O. Agoreyo and Friday E. Okonofua},
  journal={Journal of Obstetrics and Gynaecology},
  year={2005},
  volume={25},
  pages={403 - 405}
}
ditism, however, it is usually unicornuate, hypoplastic or rudimentary (Aaronson 1985). The features of feminization in form of gynaecomastia and menstruation in a patient with TH is the result of secretion of estradiol by ovarian tissue and therefore it is presumed that the female neuroendocrine axis functions normally in such individuals (Shannon and Nicolaides 1973). Bilateral gynaecomastia, presence of ovarian follicles and proliferative endometrium on histopathology was supportive evidence… 

Chromosomal Study is Must for Prepubertal Girl with Inguinal Hernia: Opportunity to Diagnose Complete Androgen Insensitivity Syndrome.

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Androgen insensitivity syndrome (AIS) was first described in details by Morris [1], who provided the descriptive terms—testicular feminization syndrome for this disorder, which is inherited as

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TLDR
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Novel (60%) and recurrent (40%) androgen receptor gene mutations in a series of 59 patients with a 46,XY disorder of sex development.

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AR gene mutation is the most frequent cause of 46,XY DSD, with a clearly higher frequency in the complete phenotype, and this series shows that 60% of mutations detected during the period 2002-2009 were novel.

Two Cases of Successful Laparoscopic Hernia Repair and Repositioning of the Testes into the Abdominal Cavity in Pediatric Patients with Androgen Insensitivity Syndrome

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TLDR
Laroscopic gonadectomy can be performed in individuals withCAI and results in rapid recovery with minimal blood loss and should be considered for all patients with CAI and intraabdominal gonads.

Bilateral laparoscopic gonadectomy in a patient with complete androgen insensitivity. A case report.

TLDR
Laroscopic gonadectomy can be performed in individuals withCAI and results in rapid recovery with minimal blood loss and should be considered for all patients with CAI and intraabdominal gonads.

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TLDR
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TLDR
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TLDR
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TLDR
A patient with complete androgen insensitivity syndrome found to have a microscopic fallopian tube at the time of gonadectomy is described and possible etiologies for the finding are discussed.

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TLDR
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TLDR
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TLDR
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