Collagen type III glomerulopathy: a new type of hereditary nephropathy

  title={Collagen type III glomerulopathy: a new type of hereditary nephropathy},
  author={Marie Claire Gubler and J. P. Dommergues and Michel Foulard and Albert Bensman and Jean Paul Leroy and Michel Broyer and Ren{\'e}e Habib},
  journal={Pediatric Nephrology},
A new type of hereditary glomerulopathy was observed in ten children presenting with early and progressive glomerular symptoms, often associated with hypertension. Light microscopy showed a diffuse increase in the mesangial matrix and generalized widening of the capillary walls. Electron-microscopic examination of renal tissue, after phosphotungstic acid treatment, revealed the presence of fibrillar collagen within the mesangial matrix and the subendothelial aspect of the glomerular basement… CONTINUE READING


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