Clinical outcomes in U.S. infants with cystic fibrosis from 2001 to 2012

@article{Hoch2018ClinicalOI,
  title={Clinical outcomes in U.S. infants with cystic fibrosis from 2001 to 2012},
  author={Heather E Hoch and Marci K. Sontag and Sharon L Scarbro and Elizabeth Juarez-Colunga and Cindie McLean and Allison Kempe and Scott D. Sagel},
  journal={Pediatric Pulmonology},
  year={2018},
  volume={53},
  pages={1492 - 1497}
}
All 50 United States implemented newborn screening (NBS) for cystic fibrosis (CF) by 2010. The purpose of this study was to evaluate trends over the decade when NBS became universal to determine current rates of malnutrition, stunting, and infection rates in U.S. infants with CF. 
Outcomes of infants born during the first 9 years of CF newborn screening in the United States: A retrospective Cystic Fibrosis Foundation Patient Registry cohort study
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The aims were to describe the outcomes of infants with CF born during the first 9 years of universal NBS, to form the basis of additional analyses and to plan quality improvement initiatives.
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This study aimed to describe the change in lung function, nutritional status, and mortality of children with CF at a single center in Cape Town, South Africa, and identify factors associated with poor lung function and mortality.
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This report summarizes research and cases related to Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) modulator therapies, inflammation and infection, epidemiology and the physiologic, and imaging assessment of disease.
Cystic fibrosis knowledge and practice among primary care physicians in southwest region, Saudi Arabia
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  • Medicine
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  • 2020
TLDR
The need for extensive educational programs for the PCPs in order to improve early recognition of CF and start the appropriate management is highlighted.
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TLDR
The decrease in prevalence of P. aeruginosa and S. aureus since 2000, coinciding with more aggressive therapeutic approach, has resulted in Aspergillus becoming the most commonly isolated pathogen in young children.
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    American journal of respiratory and critical care medicine
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TLDR
The epidemiology of lower airway infection in a modern cohort of almost 400 infants and young children diagnosed by newborn screening, followed at two Australian CF centers is reexamine, with Aspergillus as the most commonly detected pathogen from the lower airways among young children with CF.
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The case of an infant born in Illinois with a positive cystic fibrosis newborn screening with an elevated immunoreactive trypsinogen and two genetic mutations identified (F508del/F508Del) highlights the importance of performing the confirmatory sweat test prior to making a diagnosis of cystic Fibrosis.
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TLDR
An update on definitions of chronicity of infection, approaches to airway sampling to detect infection, strategies for Pseudomonas aeruginosa eradication, impact of cystic fibrosis transmembrane regualtor protein (CFTR) modulators and future challenges for clinical trials is provided.
Cystic fibrosis related diabetes: Nutrition and growth considerations.
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a Department of Women's and Children's Health, University of Liverpool, Liverpool, UK b Division of Paediatric Pulmonology, Children's Hospital, St Gallen, Switzerland c Paediatric Pneumonology and
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