Clinical neurophysiology in the diagnosis of amyotrophic lateral sclerosis: The Lambert and the El Escorial criteria

@article{Wilbourn1998ClinicalNI,
  title={Clinical neurophysiology in the diagnosis of amyotrophic lateral sclerosis: The Lambert and the El Escorial criteria},
  author={Asa J. Wilbourn},
  journal={Journal of the Neurological Sciences},
  year={1998},
  volume={160},
  pages={S25-S29}
}
  • A. Wilbourn
  • Published 1 October 1998
  • Psychology
  • Journal of the Neurological Sciences

An evaluation of neurophysiological criteria used in the diagnosis of motor neuron disease

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Fasciculation potentials in amyotrophic lateral sclerosis and the diagnostic yield of the Awaji algorithm

The Awaji algorithm has restored the value of fasciculation potentials in the diagnosis of amyotrophic lateral sclerosis and the diagnostic yield of this algorithm is lower than that of the R‐EEC.

Electrophysiologic diagnostics of very early stages of ALS.

Complex fasciculations and their origin in amyotrophic lateral sclerosis and Kennedy's disease

Combined fasciculations are distinctive in ALS, and it is hypothesized that they are triggered by a supraspinal mechanism reflecting dysfunction of descending motor pathways.

Electrodiagnostic Evaluation of Motor Neuron Disorders

Nerve conduction studies (NCS) and needle electromyography (EMG) are essential in the evaluation of suspected ALS and are primarily used to exclude any potentially treatable motor neuropathy that may mimic ALS.

Variation in the neurophysiological examination of amyotrophic lateral sclerosis in Europe

The existence of two different examination approaches, one with quantitative EMG analyses and relatively few muscles studied, and one with more muscles studied using qualitative methods was clearly confirmed in the present study.

Sensitivity and specificity of the ‘Awaji’ electrodiagnostic criteria for amyotrophic lateral sclerosis: Retrospective comparison of the Awaji and revised El Escorial criteria for ALS

The new criteria for ALS do not result in a loss of specificity and can potentially improve the sensitivity by 16%.

Needle electromyography of the frontalis muscle in patients with amyotrophic lateral sclerosis

Examining the frontalis provides useful information in establishing the diagnosis of ALS by identifying clinically evident or subclinical abnormalities in the craniobulbar region.

EFNS task force on management of amyotrophic lateral sclerosis: guidelines for diagnosing and clinical care of patients and relatives

Early diagnosis should be pursued and a number of investigations should be performed with high priority, and every effort should be made to maintain patient autonomy during the entire course of the disease.
...

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