Clinical and pathological features of pediatric dermatofibrosarcoma protuberans.

  title={Clinical and pathological features of pediatric dermatofibrosarcoma protuberans.},
  author={Tamir H Keshen and Paul S. Cederna and Van H. Savell and Charles E. Platz and Patricia Chang and Edward J. Ricciardelli},
  journal={Annals of plastic surgery},
  volume={35 6},
Dermatofibrosarcoma protuberans (DFSP) is an uncommon malignant mesenchymal tumor characterized by local invasion and recurrence. Fewer than 50 cases have been reported in the pediatric population. We reviewed our experience in the treatment of children with DFSP to define clinical and pathological characteristics. Seven pediatric patients were included in the study (mean age, 11.7 yr). Clinically, the tumors were described as firm nodules fixed to the skin but mobile over the deep fascia, with… CONTINUE READING