Chronic bullous disease of childhood and a paecilomyces lung infection in chronic granulomatous disease.

Abstract

A 12 year old boy suffering from p67-phox deficient chronic granulomatous disease presented with a bullous skin disease and a lung infection with paecilomyces species. The histopathology of a bullous lesion showed subepidermal blister formation and microabcesses containing eosinophils in the dermal papillae. By direct immunofluorescence, linear staining of IgA at the dermal-epidermal junction was detected which confirmed the clinical diagnosis of chronic bullous disease of childhood (linear IgA dermatosis).

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@article{Smitt1997ChronicBD, title={Chronic bullous disease of childhood and a paecilomyces lung infection in chronic granulomatous disease.}, author={Johannes H Sillevis Smitt and Jeanette H. W. Leusen and Helene G Stas and A. Herbert Teeuw and Ron S. Weening}, journal={Archives of disease in childhood}, year={1997}, volume={77 2}, pages={150-2} }