Chiari-like tonsillar herniation associated with intracranial hypotension in Marfan syndrome. Case report.

@article{Puget2007ChiarilikeTH,
  title={Chiari-like tonsillar herniation associated with intracranial hypotension in Marfan syndrome. Case report.},
  author={S Puget and Charles Kondageski and Alison Wray and Nathalie Boddaert and Thomas Roujeau and Federico di Rocco and M Zerah and C Sainte-Rose},
  journal={Journal of neurosurgery},
  year={2007},
  volume={106 1 Suppl},
  pages={48-52}
}
The authors describe the case of a 12-year-old girl with Marfan syndrome, sacral dural ectasia, and tonsillar herniation, who presented with headache. Initially, it was hypothesized that the headaches were secondary to the tonsillar herniation, and the patient consequently underwent surgical decompression of the foramen magnum. Postoperatively, the patient's condition did not improve, and additional magnetic resonance (MR) imaging demonstrated evidence of a cerebrospinal fluid (CSF) leak at the… CONTINUE READING