Case reports of successful pregnancy in women with maple syrup urine disease and propionic acidemia.

@article{Calcar1992CaseRO,
  title={Case reports of successful pregnancy in women with maple syrup urine disease and propionic acidemia.},
  author={S C Van Calcar and Cary O. Harding and Susan A. Davidson and Lewis A. Barness and James A. Wolff},
  journal={American journal of medical genetics},
  year={1992},
  volume={44 5},
  pages={641-6}
}
We report on 2 women with organic acidemias, one with classical maple syrup urine disease and another with mild propionic acidemia in which protein restricted diets and carnitine supplementation were successfully employed to manage pregnancies. Healthy infants were delivered without maternal metabolic decompensation. 

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