Cardiovascular autonomic dysfunction in Ehlers–Danlos syndrome—Hypermobile type

@article{Hakim2017CardiovascularAD,
  title={Cardiovascular autonomic dysfunction in Ehlers–Danlos syndrome—Hypermobile type},
  author={Alan J Hakim and Chris O'Callaghan and Inge De Wandele and Lauren E. Stiles and Alan G. Pocinki and Peter C. Rowe},
  journal={American Journal of Medical Genetics Part C: Seminars in Medical Genetics},
  year={2017},
  volume={175},
  pages={168 - 174}
}
  • A. Hakim, C. O'Callaghan, P. Rowe
  • Published 1 March 2017
  • Medicine
  • American Journal of Medical Genetics Part C: Seminars in Medical Genetics
Autonomic dysfunction contributes to health-related impairment of quality of life in the hypermobile type of Ehlers-Danlos syndrome (hEDS. [] Key Method Tests of cardiovascular function range from clinic room observation to tilt-table assessment to other laboratory investigations such as supine and standing catecholamine levels. Non-pharmacologic treatments include education, managing the environment to reduce exposure to triggers, improving cardiovascular fitness, and maintaining hydration. Although there…

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