CNS lipoma in patients with epidermal nevus syndrome.

@article{Mall2000CNSLI,
  title={CNS lipoma in patients with epidermal nevus syndrome.},
  author={V. Mall and F. Heinen and M. Uhl and E. Wellens and R. Korinthenberg},
  journal={Neuropediatrics},
  year={2000},
  volume={31 4},
  pages={
          175-9
        }
}
  • V. Mall, F. Heinen, +2 authors R. Korinthenberg
  • Published 2000
  • Medicine
  • Neuropediatrics
  • Epidermal nevus syndrome (ENS) is a congenital neurocutaneous disorder characterized by linear nevus with a significant involvement of the nervous, ophthalmological and skeletal systems. Clinical manifestations of ENS include neurological features such as mental retardation, seizures, and movement disorders which are caused by a wide range of neuropathological lesions. We describe three patients with ENS, all of whom had in addition to the characteristic features of ENS intracranial and/or… CONTINUE READING
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