CNS lipoma in patients with epidermal nevus syndrome.
@article{Mall2000CNSLI, title={CNS lipoma in patients with epidermal nevus syndrome.}, author={V. Mall and F. Heinen and M. Uhl and E. Wellens and R. Korinthenberg}, journal={Neuropediatrics}, year={2000}, volume={31 4}, pages={ 175-9 } }
Epidermal nevus syndrome (ENS) is a congenital neurocutaneous disorder characterized by linear nevus with a significant involvement of the nervous, ophthalmological and skeletal systems. Clinical manifestations of ENS include neurological features such as mental retardation, seizures, and movement disorders which are caused by a wide range of neuropathological lesions. We describe three patients with ENS, all of whom had in addition to the characteristic features of ENS intracranial and/or… CONTINUE READING
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