Budd‐Chiari syndrome in Sweden: epidemiology, clinical characteristics and survival – an 18‐year experience
@article{Rajani2009BuddChiariSI, title={Budd‐Chiari syndrome in Sweden: epidemiology, clinical characteristics and survival – an 18‐year experience}, author={Rupesh Rajani and T Melin and Einar S. Bj{\"o}rnsson and Ulrika Broomé and Per Sangfelt and {\AA}ke Danielsson and Anders Gustavsson and Olof Grip and Hans Svensson and Lars L{\"o}{\"o}f and Sven Wallerstedt and Sven Alm{\'e}r}, journal={Liver International}, year={2009}, volume={29} }
Background: The exact incidence and prevalence of Budd‐Chiari syndrome (BCS) is unknown in the general population. Published reports differ in terms of the clinical characteristics, effects of therapy and survival.
128 Citations
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- 2016
This study aimed to elucidate the nationwide population‐based incidence, prevalence, complications, case fatalities and direct medical cost of Budd–Chiari syndrome in South Korea from 2009 to 2013.
Clinical features and etiology of Budd–Chiari syndrome in Chinese patients: A single‐center study
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The clinical features and etiology of patients with incident BCS in China prospectively vary from region to region, and there is lack of large sample studies about BCS.
Rotterdam score predicts early mortality in Budd‐Chiari syndrome, and surgical shunting prolongs transplant‐free survival
- MedicineAlimentary pharmacology & therapeutics
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This data indicates that among children born with Budd–Chiari syndrome, the likelihood of survival is low, but the chances of survival among those born with a second syndrome are high.
Review article: a multidisciplinary approach to the diagnosis and management of Budd‐Chiari syndrome
- MedicineAlimentary pharmacology & therapeutics
- 2019
Budd‐Chiari syndrome (BCS) is a rare but fatal disease caused by obstruction in the hepatic venous outflow tract.
Early radiological intervention and haematology screening is associated with excellent outcomes in Budd–Chiari syndrome
- MedicineInternal medicine journal
- 2017
Budd–Chiari syndrome (BCS) is a rare and life‐threatening disorder, resulting from thrombosis of the hepatic veins. Various treatments, including pharmacological, radiological and surgical…
Pregnancy outcomes in women with Budd–Chiari syndrome or portal vein thrombosis – a multicentre retrospective cohort study
- MedicineBJOG : an international journal of obstetrics and gynaecology
- 2021
To evaluate current practice and outcomes of pregnancy in women previously diagnosed with Budd–Chiari syndrome and/or portal vein thrombosis, with and without concomitant portal hypertension.
Review article: the aetiology of primary Budd–Chiari syndrome – differences between the West and China
- MedicineAlimentary pharmacology & therapeutics
- 2016
Considering the discrepancy in the clinical profiles and preferred treatment selection of primary BCS between the West and China, understanding its aetiology in these two different regions is very important.
Budd-Chiari Syndrome: The Western Perspective
- Medicine
- 2018
Primary Budd-Chiari syndrome (BCS) is defined as hepatic venous outflow obstruction from small hepatic veins to the inferior vena cava (IVC), due to thrombosis or fibrous stenosis of these veins. In…
Budd–Chiari Syndrome: East versus West
- MedicineBudd-Chiari Syndrome
- 2019
Budd–Chiari syndrome is an uncommon cause of liver disease, which is being diagnosed more frequently with better diagnostic techniques especially in the East, and excellent responses to radiological interventional techniques like angioplasty and transjugular intrahepatic portosystemic shunt have resulted in excellent long-term survivals in both the East and the West.
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