Brooke-Spiegler syndrome with associated pegged teeth.

  title={Brooke-Spiegler syndrome with associated pegged teeth.},
  author={Ryan M Carlson and Lori Haddad and John C Pui},
  volume={82 5},
The occurrence of cylindromas, trichoepitheliomas, and spiradenomas completes the triad for Brooke-Spiegler syndrome (BSS). This combination represents a rare genetic syndrome with tumors expressing adnexal differentiation. Malignant transformation is rare but reported, and surgical excision is warranted to prevent turban tumor formation of the scalp… CONTINUE READING