Botryoid rhabdomyosarcoma of the biliary tract in children: a unique case report.

@article{Zampieri2006BotryoidRO,
  title={Botryoid rhabdomyosarcoma of the biliary tract in children: a unique case report.},
  author={Nicola Zampieri and F. S. Camoglio and Michele Corroppolo and Mariangela Cecchetto and Sara Ornis and Alberto Ottolenghi},
  journal={European journal of cancer care},
  year={2006},
  volume={15 5},
  pages={
          463-6
        }
}
Rhabdomyosarcoma (RMS) is the most common tumour of the biliary tree in childhood. In children, it is a rare lesion, accounting for about 1% of all RMS. Hepatobiliary botryoid RMS is a disease affecting young children at a median age of about 3 years. In literature, the radiological findings of hepatobiliary RMS have been described in small series and some case reports. In this case report, we present a rare case of RMS of the extrahepatic biliary tree initially diagnosed as a choledochal cyst. 
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Botryoid rhabdomyosarcoma of common bile duct: Diagnostic imaging features of an unusual pathology: Case report and review
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The key to diagnosis is to distinguish solid component of the tumor from organized sludge seen in choledochal cyst, which plays a vital role for preoperative staging as well.
Rhabdomyosarcoma of the common bile duct: an unusual cause of obstructive jaundice in a child.
TLDR
The role of surgery in the small-sized tumor and the role of endoscopic retrograde cholangiopancreatography (ERCP) in the diagnosis and relief of biliary obstruction before total excision are emphasized.
Rhabdomyosarcoma of Biliary Tract Misdiagnosed as Choledocal Cyst-Two Cases and Review of Literature
TLDR
Two cases of children who presented to us with obstructive jaundice and palpable liver were misdiagnosed as choledochal cyst on imaging studies; however, intraoperative and histopathological features confirmed the diagnosis of rhabdomyosarcoma.
A Rare Intra-Abdominal Rhabdomyosarcoma in a Child (Case Report and Review of Literature)
TLDR
This is a case report of a rhabdomyosarcoma of the mesentery in an 8-year-old girl, extremely rare and only few cases were reported in the literature.
Rhabdomyosarcoma of the mesentery in an infant
TLDR
A case report of a rhabdomyosarcoma of the mesentery in a 4 month-old male infant and CT-scan is presented.
Application of ERCP and Spyglass Technique in Diagnosis of Pediatric Botryoid Rhabdomyosarcoma of the Biliary Duct
TLDR
A case of embryonal rhabdomyosarcoma involving the common and right hepatic ducts in a female child and treated with right liver lobectomy following chemotherapy for control positive resection margins is reported.
Rhabdomyosarcoma arising within the biliary tract mimicking a choledochal cyst: A case report
TLDR
A patient with biliary RMS initially thought to be a choledochal cyst with intraluminal cystic debris (biliary sludge) that was diagnosed by frozen section examination during cyst resection is presented and subsequently treated with post-operative chemotherapy and radiation.
Embryonal rhabdomyosarcoma of the ampulla of Vater in early childhood: report of a case and review of literature.
Biliary tract rhabdomyosarcoma: a report from the Soft Tissue Sarcoma Committee of the Associazione Italiana Ematologia Oncologia Pediatrica
TLDR
Better outcomes in this series were associated with the feasibility of conservative surgery due to the favorable location of the tumor, in particular in the common bile duct, which might obviate the need for demolitive surgery or liver transplant, which were linked to worse outcomes in the series.
Diagnostic and therapeutic role of endoscopic retrograde cholangiopancreatography in biliary rhabdomyosarcoma.
TLDR
Endoscopic retrograde cholangiopancreatography was successfully used both diagnostically and therapeutically in a 3-year-old boy with BRMS, thus obviating the need for surgery and its attendant risks of morbidity and mortality.
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