Biochemistry of peroxisomes in health and disease
@article{Singh2004BiochemistryOP, title={Biochemistry of peroxisomes in health and disease}, author={Inderjit Singh}, journal={Molecular and Cellular Biochemistry}, year={2004}, volume={167}, pages={1-29} }
The ubiquitous distribution of peroxisomes and the identification of a number of inherited diseases associated with peroxisomal dysfunction indicate that peroxisomes play an essential part in cellular metabolism. Some of the most important metabolic functions of peroxisomes include the synthesis of plasmalogens, bile acids, cholesterol and dolichol, and the oxidation of fatty acids (very long chain fatty acids > C22, branched chain fatty acids (e.g. phytanic acid), dicarboxylic acids…
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