Autoimmune Vasculitis in a Child Following Tetralogy of Fallot Repair in Uganda

  • Published 2017

Abstract

Tetralogy of Fallot is the most common cyanotic congenital heart disease worldwide [1]. Among other conotruncal abnormalities, 13-16% of Tetralogy of Fallot individuals are reported to have 22q11.2 deletion syndrome which is characterized by thymic hypoplasia, endocrine abnormalities and hypocalcaemia [2]. Individuals with micro deletion 22q11.2 deletion syndrome are prone to auto immune disorders. Defects in thymic development predispose them to impaired immune function especially T cell deficiency [3]. However autoimmune vasculitis has not been well documented in children with Tetralogy of Fallot. We report on an eleven-year-old child post Tetralogy of Fallot repair who presented with persistent fevers and an over whelming infection.

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Cite this paper

@inproceedings{2017AutoimmuneVI, title={Autoimmune Vasculitis in a Child Following Tetralogy of Fallot Repair in Uganda}, author={}, year={2017} }