Asymptomatic atrophy of the temporal median raphe of the retina associated with cerebral vasculopathy in homozygous sickle cell disease.

@article{Robert2012AsymptomaticAO,
  title={Asymptomatic atrophy of the temporal median raphe of the retina associated with cerebral vasculopathy in homozygous sickle cell disease.},
  author={Matthieu P. A. Robert and Isabelle Ingster-Moati and Olivier Roche and Nathalie Boddaert and Marianne de Montalembert and Valentine Brousse and Manoelle Kossorotoff and J L Dufier and C{\'e}line Faure},
  journal={Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus},
  year={2012},
  volume={16 4},
  pages={394-7}
}
A 13-year-old girl with homozygous sickle cell disease was referred for vision loss in her left eye of 1 year's duration. Clinical findings were consistent with a past retinal arterial occlusion. In the asymptomatic right eye, spectral domain optical coherence tomography showed a severe atrophy of the inner retinal layers of the temporal median raphe; a significant internal carotid stenosis was also present. We hypothesize that specific atrophy of the retinal temporal median raphe resulted from… CONTINUE READING