Association of inflammatory pseudotumor of the liver and Papillon-Lefevre syndrome--case report.

@article{Czauderna1999AssociationOI,
  title={Association of inflammatory pseudotumor of the liver and Papillon-Lefevre syndrome--case report.},
  author={Piotr Czauderna and Katarzyna Sznurkowska and Maria Korzon and Andrzej Roszkiewicz and Czeslaw Stoba},
  journal={European journal of pediatric surgery : official journal of Austrian Association of Pediatric Surgery ... [et al] = Zeitschrift fur Kinderchirurgie},
  year={1999},
  volume={9 5},
  pages={343-6}
}
A case of hepatic inflammatory pseudotumor mimicking malignancy in a 4-year-old girl with the Papillon-Lefevre syndrome (PLS) is reported. Only recently, an association between this inherited syndrome and liver abscesses has been found. Its possible pathogenesis is discussed and immunologic defects resulting from the Papillon-Lefevre syndrome are presented… CONTINUE READING