Association of cerebellopontine angle atypical teratoid/rhabdoid tumors with acute facial nerve palsy in infants.

Abstract

Atypical teratoid/rhabdoid tumors (AT/RTs) are highly malignant CNS tumors found almost exclusively in childhood. Although essentially universally fatal when incompletely resected, prompt diagnosis followed by early chemoradiation can improve outcomes. An AT/RT can occur extraaxially at the cerebellopontine angle (CPA) and cause acute cranial nerve deficits as the presenting sign. The authors report a series of 3 children who presented with isolated acute facial nerve palsies and in whom subsequent diagnosis of a CPA AT/RT was made. The authors propose that in young children whose presenting symptom is an acute facial nerve palsy with a CPA tumor, AT/RT should be highly suspected.

DOI: 10.3171/2013.10.PEDS13292

Cite this paper

@article{Siu2014AssociationOC, title={Association of cerebellopontine angle atypical teratoid/rhabdoid tumors with acute facial nerve palsy in infants.}, author={Alan Siu and Michaela Lee and Robert N . Rice and John S. Myseros}, journal={Journal of neurosurgery. Pediatrics}, year={2014}, volume={13 1}, pages={29-32} }