Arrhythmogenic cardiomyopathy in a patient with Noonan syndrome.


Arrhythmogenic ventricular cardiomyopathy (AVC) presents with fat replacement of the myocardium, most commonly of the right ventricle, and ventricular arrhythmias. We report an 11-year-old boy with Noonan syndrome, ventricular arrhythmias, and an ultrasound depicting hypertrophy of the ventricular septum with subaortic stenosis. A surgical resection of the… (More)
DOI: 10.3109/15513811003777326


Cite this paper

@article{Altamirano2010ArrhythmogenicCI, title={Arrhythmogenic cardiomyopathy in a patient with Noonan syndrome.}, author={Eugenia M Altamirano and Ricardo Drut}, journal={Fetal and pediatric pathology}, year={2010}, volume={29 3}, pages={158-64} }