Aplasia cutis congenita. Case report.

@article{Nichols1996AplasiaCC,
  title={Aplasia cutis congenita. Case report.},
  author={D D Nichols and Alberta Bottini},
  journal={Journal of neurosurgery},
  year={1996},
  volume={85 1},
  pages={
          170-3
        }
}
The authors report the use of intraoperative tissue expansion in the treatment of a neonate with aplasia cutis congenita, a congenital defect of the scalp and skull. The case for immediate surgical intervention is presented, and intraoperative tissue expansion and cranioplasty are recommended as components of an effective surgical approach. 
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Aplasia Cutis Congenita Scalp Presenting with Life Threatening Hemorrhage: A Case Report
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A 5-day-old neonate with Aplasia cutis congenita was received in a state of shock due to tremendous blood loss from the superior sagittal sinus and resuscitated immediately followed by closure of the superior Sagittal Sinus and flap coverage to the defect as a life saving procedure.
Conservative Treatment of a Patient with Epidermolysis Bullosa Presenting as Bart Syndrome: A Case Report
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In a case of a newborn male with aplasia cutis congenita on the lower limb, the wound was completely epithelialized, but a hypopigmented scar remained in the limb.
Aplasia cutis congenital. A case report
TLDR
A case of ACC is reported, a rare congenital disorder that commonly affects the scalp that presents as a solitary lesion but with multiple lesions also were reported.
Management of aplasia cutis congenita in a non-scalp location.
TLDR
The conservative management of a newborn with extensive aplasia cutis congenita of the thighs associated with a monochorionic co-twin foetus papyraceous is reported, and the skin defects on both thighs healed in 38 days.
Aplasia cutis congenita: a rare case with extensive symmetrically distributed lesions.
TLDR
An interesting presentation of AC along with the histopathological features in a neonate with extensive lesions over scalp as well as in bilaterally symmetrical areas over trunk and thighs is reported.
[Vertex aplasia cutis congenita with bone defect: Management synthesis and review of the literature].
First Case Report of an Infant with Aplasia Cutis Congenita of Scalp and Myelomeningocele
TLDR
This is the first case of a newborn boy with ACCS and myelomeningocele whose evolution with hydrocephalus has brought a serious paradigm of using a shunt in the presence of tissue expanders, and therapeutic strategies and challenges with this disease are described.
Aplasia Cutis Congenita of the Scalp, Composite Type: The Criticality and Inseparability of Neurosurgical and Plastic Surgical Management
TLDR
Early aggressive surgical management with scalp rotation flaps has a low rate of complications, provides satisfactory functional and esthetic outcome, minimizes hospital stays, and should provide cost-effective care by reduction of the time to secure wound closure.
Aplasia cutis congenita of the scalp.
TLDR
An infant with a large full thickness skin and skull defect on the scalp and other malformations which proved to be fatal is read with great interest by Yilmaz et al.
Aplasia cutis congenita of the scalp: is there a better treatment strategy?
TLDR
Three newborns with ACC of the scalp, two large defects and a medium one, respectively, treated conservatively and surgically are reported, suggesting that conservative treatment should be performed for initial management in newborns.
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References

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TLDR
The use of rotation skin flaps is reported as the preferable plastic procedure for congenital scalp defects and the need for immediate repair of large defects within a few hours of birth is emphasized.
Total reconstruction of aplasia cutis congenita involving scalp, skull, and dura.
TLDR
Tissue expansion was successfully employed on two occasions: first to construct a well-vascularized space to sustain multiple rib grafts for cranial reconstruction and then to develop adequate quantities of scalp and forehead for total coverage.
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Nine patients with aplasia cutis congenita were treated in our department during the past 30 years. Of these, 1 patient died due to uncontrolled hemorrhage and 1 patient was operated on by using a…
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TLDR
The area in the scalp was rapidly ulcerated and was treated three days after birth with debridement and coverage with a silicone elastomer membrane, and three weeks later the membrane was excised and the area successfully grafted with split-thickness skin.
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TLDR
Three children born with non-syndromic ACC are reported, of which one was not acknowledged immediately after birth and treated conservatively or with standard wound/encephalocele treatment with satisfying results.
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TLDR
A male newborn with a large scalp and skull defect and a cervical meningocele was transferred to the neonatal intensive care unit of the North Carolina Baptist Hospital and treated thrice daily with the topical application of bacitracin ointment and circumferential dressings.
Surgical management of aplasia cutis congenita.
TLDR
The successful outcome suggests that the present philosophy of early surgical closure being essential for survival in infants with large cranial defects can be altered and, in fact, permanent full-thickness flaps may be designed, tested for viability, and delayed while homograft skin protects the infant's brain from infection and thrombosis.
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TLDR
A nonoperative approach to the management of congenital scalp and skull defects is reported, which emphasizes the natural course that some of these lesions may follow.
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